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Table 2 Post-mortem tissue donor demographics

From: Blood-spinal cord barrier leakage is independent of motor neuron pathology in ALS

Group

Case code

Age (y)

Sex

Post-mortem delay (h)

Cause of death

Control (n = 5)

H232

89

F

28.5

Multiple stroke, dementia

H233

83

F

18

Acute renal failure, bowel cancer

H234

86

M

3

Stroke, dementia

H235

83

M

21

Hypothermia

H236

96

F

15

General inanition

Mean (± SD)

87.4 ± 5.4

F/M: 3/2

17.1 ± 9.3

 

Group

Case code

Age (y)

Sex

Post-mortem delay (h)

sALS/fALS (genotype)

Site of onset

ALS (n = 13)

MN7

55

F

56

sALS

Upper limb

MN10

46

M

24

sALS

Lower limb

MN11

77

F

18

fALS

Lower limb

MN12

49

M

34

sALS

Respiratory

MN13

55

M

10

sALS

Upper limb

MN14

59

F

19

fALS

Bulbar

MN15

54

F

18

sALS

FTD

MN16

69

M

16.5

sALS

Upper limb

MN18

53

F

12

fALS (C9ORF72)

Lower limb

MN20

85

M

15

sALS

Lower limb

MN21

59

F

17.5

fALS

Lower limb

MN22

64

F

9

sALS

Upper limb

MN23

79

F

27

fALS (C9ORF72)

Lower limb

Mean (± SD)

61.8 ± 12.2

F/M: 8/5

21.2 ± 12.5

  
  1. sALS sporadic ALS, fALS familial ALS, FTD frontotemporal dementia