Table 1 Distribution and density of p62-positive intranuclear inclusions in the proband

Cerebrum

Sympathetic ggl

3

2

Frontal^a

1/n.a.

1/1

Dorsal root ggl

3

2

Motor^a

2/n.a.

1/1

Myenteric ggl

2

2

Temporal^a

2/n.a.

2/1

Parietal^a

1/n.a.

1/1

Visceral organs

Occipital^a

2/n.a.

1/1

Kidney

Renal tubule

Glomerulus

Hippocampus^b

2/3/1

1/1/1

2

2

Amygdala

2

1

Liver

Hepatocyte

NBM

1

1

0

Caudate/putamen

1/1

1/1

Pancreas

Acinar cell

Ductal cell

Globus pallidus i/e

1/1

1/1

1

1

Thalamus

2

1

Adrenal

Cortex

Medulla

Brainstem

1

1

Midbrain tectum

2

1

Heart

Muscle cell

Oculomotor nuc

2

2

1

Red nuc

2

2

Skeletal muscle

Muscle cell

Substantia nigra

3

2

0

Locus ceruleus

2

1

Facial nuc

2

1

Somatic cells

Adipocyte

EC

SMC

Pontine nuc

1

1

1

1

2

Hypoglossal nuc

2

0

IO

2

1

Cerebellum^c

1/n.a./0

1/1/1

Spinal cord

Anterior horn

2

1

IML

2

0

Clarke’s column

0

0

Posterior horn

2

1

Wm

0

1

Others

Ependymal cell

Choroid plexus

0

2