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Table 1 Case demographics of cases used in the study

From: Heterogeneous nuclear ribonucleoproteins R and Q accumulate in pathological inclusions in FTLD-FUS

Cases

Disease group

Age at onset

Age at death

Disease duration

Gender

Post-mortem delay (hours)

1

FTLD-FUS

41

43

2

F

55

2

FTLD-FUS

44

46

2

M

96

3

FTLD-FUS

63

59

6

F

2

4

FTLD-FUS

43

46

3

F

30

5

FTLD-FUS

69

72

3

F

90

6

FTLD-FUS

66

69

3

F

102

7

FTLD-FUS

49

55

6

F

3.5

8

FTLD-FUS

43

53

10

F

96

9

FTLD-FUS

55

58

3

F

N/A

10

FTLD-FUS

40

51

11

M

12

11

FTLD-FUS

44

51

7

M

24

12

FTLD-FUS

47

53

6

M

5

13

FTLD-FUS

51

60

9

M

48

FTLD-FUS summary

50 (9.5)

55 (8.5)

5.5 (3)

5 M:8F

47 (40)

14

FTLD-TDP A

66

74

8

F

86

15

FTLD-TDP A

43

45

2

M

26

16

FTLD-TDP A

53

63

10

M

77

17

FTLD-TDP A

62

68

6

M

99

18

FTLD-TDP A

58

67

9

F

115

19

FTLD-TDP A

56

67

11

F

85.5

20

FTLD-TDP A

57

62

5

F

63

21

FTLD-TDP A

66

71

5

M

52

22

FTLD-TDP A

58

66

8

F

107

23

FTLD-TDP A

47

53

6

M

34

24

FTLD-TDP A

53

61

8

M

72.5

25

FTLD-TDP A

57

62

5

M

93

26

FTLD-TDP A

62

72

10

M

97.5

27

FTLD-TDP A

49

55

6

M

29

28

FTLD-TDP A

75

78

3

F

36

29

FTLD-TDP A

83

87

4

F

69

30

FTLD-TDP A

57

63

6

F

85

31

FTLD-TDP A

72

79

7

F

50

32

FTLD-TDP A

62

68

6

F

100

FTLD-TDP A summary

59 (10)

66 (10)

6.6 (2.4)

9 M:10F

71 (28)

33

FTLD-TDP B

67

69

2

M

70

34

FTLD-TDP B

63

67

4

F

45.5

35

FTLD-TDP B

63

83

20

F

45

FTLD-TDP B summary

64.3 (2.3)

73 (8.7)

8.6 (9.8)

1 M:2F

53.5 (14)

36

FTLD-TDP C

58

73

15

F

38

37

FTLD-TDP C

59

73

14

F

84

38

FTLD-TDP C

64

78

14

M

27

39

FTLD-TDP C

64

74

10

M

19

40

FTLD-TDP C

50

65

15

M

52

41

FTLD-TDP C

61

66

5

M

71

42

FTLD-TDP C

44

67

23

M

76

FTLD-TDP C summary

57.1 (7.5)

70.8 (4.9)

13.7 (5.5)

5 M:2F

52 (25)

43

Control

80

N/A

N/A

M

16

44

Control

79

N/A

N/A

F

89

45

Control

80

N/A

N/A

F

49

46

Control

93

N/A

N/A

F

30

47

Control

73

N/A

N/A

F

24

48

Control

83

N/A

N/A

F

20

Control summary

81.3 (6.6)

N/A

N/A

1 M:5F

14 (3.5)