Group
|
M/F
|
Age at onset (y)
|
Age at Death (y)
|
Duration of illness (y)
|
---|
C9ORF72 FTD
|
7/1
|
61.1 ± 8.5
|
67.6 ± 7.0
|
6.5 ± 3.0
|
C9ORF72 FTD + MND
|
2/4
|
58.8 ± 6.1
|
64.7 ± 5.8
|
5.8 ± 6.2
|
C9ORF72 MND
|
6/1
|
55.8 ± 8.6
|
57.6 ± 7.6
|
2.8 ± 1.7
|
All C9ORF72 cases
|
15/6
|
58.9 ± 7.8
|
63.4 ± 7.9
|
5.2 ± 4.1
|
GRN FTD
|
7/5
|
60.8 ± 5.9
|
69.7 ± 3.9
|
8.8 ± 3.8
|
Non-mutational FTD
|
2/2
|
60.8 ± 11.9
|
68.0 ± 15.6
|
7.3 ± 4.1
|
Non-mutational FTD + MND
|
9/1
|
59.3 ± 7.0
|
65.4 ± 8.2
|
6.2 ± 3.8
|
All non-mutational FTD
|
11/3
|
59.6 ± 12.7
|
63.4 ± 13.6
|
2.4 ± 1.1
|
Non-mutational MND
|
12/8
|
59.7 ± 8.2
|
66.1 ± 10.2
|
6.5 ± 3.8
|
- FTD = Frontotemporal Dementia, FTD + MND + Frontotemporal dementia and Motor Neurone disease, MND = Motor Neurone Disease.