Progressive multifocal fibrosing neuropathy: description of a novel disease

Table 1 Differences in the clinical features of selected systemic fibrotic diseases with Progressive Multifocal Fibrosing Neuropathy

	Nerve entrapment	Raynaud’s phenomenon	Sclerodactyly	Skin fibrosis	Lung/heart involvement	ANA/specific Autoantibodies
Progressive Multifocal Fibrosing Neuropathy	Present	Present	Absent	Absent	Absent	Absent
Systemic Sclerosis	Present	Present	Present	Present,	Present, frequently	Present
Eosinophilia Myalgia Syndrome	Present	Absent	Present	Present, diffuse	Present	Absent
Nephrogenic Systemic Fibrosis	Present	Absent	Absent	Present, varies	Present	Absent
Toxic Oil Syndrome	Present	Rare	Present	Present	Present	Absent

ISSN: 2051-5960