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Table 5 Outcomes of the included studies

From: Right temporal variant frontotemporal dementia is pathologically heterogeneous: a case-series and a systematic review

 

Publications

N

Institution

Country

Macroscopy (atrophy pattern)

Microscopy

1

[52]

1

UCL

UK

Frontotemporal predominant R-FT = L-FT

TDP type C + CTD

2

[69]

1

MCCN

UK

Temporal predominant R-T = L–T

Tau-PSP + TDP type A

3

[54]

9

UCSF

USA

Frontotemporal predominant R-FT = L-FT (n = 1)

TDP-C: N.A

Tau-PiD (n = 1)

TDP type C (n = 8)

4

[61]

1

UCSF

USA

N.A

TDP type C + Tau-PSP

5

[63]

1

UCL

UK

Temporal predominant R-T = L–T

TDP type A

6

[64]

1

Helsinki University

Finland

Frontotemporal predominant R-FT = L-FT

TDP type A

7

[70]

1

Cambridge Brain Bank

UK

Temporal predominant R-T = L–T

Tau-MAPT

8

[55]

1

UCL

UK

Frontotemporal predominant R-FT > L-FT

Tau-GGT

9

[67]

1

UCSF

USA

Frontotemporal predominant R-FT > L-FT

TDP type A-B + AD + 4R tau

10

[38]

7

Mayo Clinic

USA

Individual data N.A. Overall, temporal predominant

TDP type C (n = 1)

TDP type C + CTD (n = 6)

11

[56]

2

Mayo Clinic

USA

N.A

TDP type B + MND* (n = 1)

TDP type B + MND* + AD (n = 1)

12

[66]

1

UCSF

USA

Striatal predominant

FUS

13

[68]

1

Uppsala University

Sweden

Temporal predominant R-T > L–T

TDP type B + MND*

14

[60]

1

UCL

UK

N.A

TDP type A-B

15

[62]

1

Tokyo IP

Japan

Temporal predominant R-T > L–T

TDP type B + MND*

16

[65]

1

Tokyo IP

Japan

Temporal predominant R-T > L–T

TDP type A-B + MND*

17

[4]

1

UCL

UK

N.A

AD + DLB (n = 1)

18

[38]

8

Mayo clinic

USA

N.A

Tau-PiD (n = 1)

Tau-MAPT (n = 7)

19

[59]

2

UCL

UK

N.A

TDP type A-B (n = 2)

20

[71]

1

Aichi University

Japan

Frontotemporal predominant R-FT = L-FT

TDP type A-B + AD

21

[58]

1

Northwestern

University

USA

N.A

TDP type A-B + MND*

  1. TDP: TAR DNA-binding protein 43; TAU: tau protein; CTD: corticospinal tract degeneration; MND: motor neuron disease; MAPT: microtubule associated protein; FUS: fused in sarcoma protein; PiD: Pick’s disease; PSP: progressive supranuclear palsy; FTLD-U: frontotemporal lobar degeneration with tau-negative, ubiquitin-immunoreactive pathology; AD: Alzheimer’s disease; DLB: dementia with Lewy bodies; UCL: University College London; UCSF: University of California San Francisco; FTD: frontotemporal dementia; MCCN: Manchester Centre for Clinical Neurosciences; IP: institute of psychiatry; VAPSHCS: Veterans Affairs Puget Sound Health Care System
  2. *Clinically diagnosed with FTD + MND