Right temporal variant frontotemporal dementia is pathologically heterogeneous: a case-series and a systematic review

Table 4 Pathological features of diagnostic groups

Case	Diagnosis	Macroscopic analysis (atrophy pattern)	Microscopic analysis
1	rtvFTD	Frontotemporal predominant R-FT > L-FT	FTLD-TDP type B + MND
2	rtvFTD	Frontotemporal predominant R-FT = L-FT	FTLD-TDP type E
3	rtvFTD	Frontotemporal predominant R-FT > L-FT	FTLD-tau-MAPT
4	rtvFTD	Frontotemporal predominant R-FT = L-FT	FTLD-FUS
5	rtvFTD	Temporal predominant R-T = L–T	FTLD-TDP type C

rtvFTD: right temporal variant frontotemporal dementia; svPPA: semantic variant primary progressive aphasia; R: right; L: left; F: frontal; T: temporal; TDP: TAR DNA-binding protein 43; TAU: tau protein; MND: motor neuron disease; MAPT: microtubule associated protein; FUS: fused in sarcoma protein; PiD: Pick’s disease

ISSN: 2051-5960