Table 1 Clinico-pathological characteristics of cPNET
Variable | CNS_NBL (20) | GBM_G34 (22) | GBM_MYCN (18) | EPN_RELA (24) |
|---|---|---|---|---|
Age (range) | 8 (4–16) | 14 (12–18) | 8 (3–17) | 9 (3–17) |
Gender M/F | 25%/75% | 70%/30% | 60%/40% | 50%/50% |
M 2–3 stage | 30% | 20% | 25% | 20% |
Resection GTR/NTR | 50%/50% | 60%/40% | 50%/50% | 60%/40% |
Recurrence | 3 (15%) | 20 (91%) | 17 (94%) | 18 (75%) |
5-year PFS | 80% | 0 | 0 | 20% |
Death | 2 (10%) | 16 (73%) | 16 (89%) | 11 (46%) |
5 year OS | 82% | 16% | 0 | 72% |
Synaptophysin (pos) | 76% | 83% | 24% | 12% |
OLIG1 (pos) | 78% | 22% | 56% | 10% |
MAP2 (pos) | 82% | 77% | 22% | 34% |
L1CAM (pos) | 22% | 44% | 38% | 100% |
EMA (dot-like) | 18% | 34% | 47% | 58% |