| FTLD | FTLD-ALS | ALS |
---|---|---|---|
N (% male) | 23 (52%) | 23 (57%) | 15 (53%) |
Age at death (year) | 65 ± 8a | 67 ± 8a | 71 ± 8 |
Age at onset (year) | 59 ± 8a | 63 ± 8a | 70 ± 7 |
Disease duration (year) | 6 ± 4a | 4 ± 3 | 2 ± 2 |
Postmortem delay (hours) | 25 ± 23 | 25 ± 17 | 22 ± 10 |
bvFTD/SD/PNFA/FTD unspecified/AD (n) | 21/0/0/1/1 | 17/2/2/1/1 | N/A |
C9ORF72 carrier % (n) | 48% (11)a | 39% (9)a | 0% (0) |
GRN carrier % (n) | 35% (8)a | 0% (0)b | 0% (0)b |