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Table 3 The demographic data and major clinical features of all FTLD cases

From: Chorea as a clinical feature of the basophilic inclusion body disease subtype of fused-in-sarcoma-associated frontotemporal lobar degeneration

  FTLD-FUS FTLD-TDP FTLD-tau Unclassified
  BIBD (n = 6) NIFID (n = 2) aFTLD-U (n = 1) Unclassified (n = 1) Type A (n = 4) Type B (n = 17) Type C (n = 10) Unclassified (n = 1) Pick (n = 18) FTDP-17 (n = 1) CBD (n = 4) PSP (n = 4) Unclassified (n = 2) (n = 1)
Sex [male/female(%)] 3/3 (50.0) 1/1 (50.0) 1/0 (100.0) 0/1 (0) 2/2 (50.0) 7/10 (41.2) 6/4 (60.0) 1/0 (100.0) 10/8 (55.6) 1/0 (100.0) 1/3 (0.25) 3/1 (0.75) 0/2 (0) 1/0
onset (y) 49.5 ± 12.1 48 ± 26.9 39 30 53 ± 16.4 58.9 ± 11.0 55.6 ± 3.5 75 56.5 ± 10.9 51 61 ± 3.4 52.5 ± 10.6 53 ± 5.7 46
duration (y) 8 ± 4.6 6.9 ± 1.6 13 15 9.5 ± 7.9 2.6 ± 1.4 12.5 ± 4.8 5.1 8.3 ± 4.5 8 5.5 ± 2.6 13 ± 7.1 6.5 ± 2.1 3.1
clinical diagnosis as bvFTD[n(%)] 5(83.3) 1(50.0) 1(100.0) 1(100.0) 3(75.0) 2(11.8) 5(50.0) 0(0) 12(66.7) 1(100.0) 3(75.0) 1(25.0) 1(50.0) 1(100.0)
involuntary movements[n(%)] 3(50.0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0) 0(0)
mortor signs[n(%)] 1(16.7) 2(100.0) 0(0) 0(0) 3(75.0) 7(41.2) 7(70.0) 0(0) 2(11.1) 0(0) 0(0) 0(0) 1(50.0) 0(0)