Table 3 The demographic data and major clinical features of all FTLD cases
| Â | FTLD-FUS | FTLD-TDP | FTLD-tau | Unclassified | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
|  | BIBD (n = 6) | NIFID (n = 2) | aFTLD-U (n = 1) | Unclassified (n = 1) | Type A (n = 4) | Type B (n = 17) | Type C (n = 10) | Unclassified (n = 1) | Pick (n = 18) | FTDP-17 (n = 1) | CBD (n = 4) | PSP (n = 4) | Unclassified (n = 2) | (n = 1) |
Sex [male/female(%)] | 3/3 (50.0) | 1/1 (50.0) | 1/0 (100.0) | 0/1 (0) | 2/2 (50.0) | 7/10 (41.2) | 6/4 (60.0) | 1/0 (100.0) | 10/8 (55.6) | 1/0 (100.0) | 1/3 (0.25) | 3/1 (0.75) | 0/2 (0) | 1/0 |
onset (y) | 49.5 ± 12.1 | 48 ± 26.9 | 39 | 30 | 53 ± 16.4 | 58.9 ± 11.0 | 55.6 ± 3.5 | 75 | 56.5 ± 10.9 | 51 | 61 ± 3.4 | 52.5 ± 10.6 | 53 ± 5.7 | 46 |
duration (y) | 8 ± 4.6 | 6.9 ± 1.6 | 13 | 15 | 9.5 ± 7.9 | 2.6 ± 1.4 | 12.5 ± 4.8 | 5.1 | 8.3 ± 4.5 | 8 | 5.5 ± 2.6 | 13 ± 7.1 | 6.5 ± 2.1 | 3.1 |
clinical diagnosis as bvFTD[n(%)] | 5(83.3) | 1(50.0) | 1(100.0) | 1(100.0) | 3(75.0) | 2(11.8) | 5(50.0) | 0(0) | 12(66.7) | 1(100.0) | 3(75.0) | 1(25.0) | 1(50.0) | 1(100.0) |
involuntary movements[n(%)] | 3(50.0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) | 0(0) |
mortor signs[n(%)] | 1(16.7) | 2(100.0) | 0(0) | 0(0) | 3(75.0) | 7(41.2) | 7(70.0) | 0(0) | 2(11.1) | 0(0) | 0(0) | 0(0) | 1(50.0) | 0(0) |