Protein | A1 | A2 | A3 |
---|---|---|---|
Z-disc (−associated) proteins | |||
 Myotilin | ↑↑↑ | ↓ | ↓∕- |
 Filamin C | ↑↑∕↑↑↑ | ↑↑↑ | ↑↑∕↑↑↑ |
 N-RAP | ↑↑ | ↑↑↑ | ↑↑ |
 XIRP2 | ↑↑∕↑↑↑ | ↑↑↑ | ↑ |
 Xin | ↑↑∕↑↑↑ | ↑↑↑ | (↑) |
 Obscurin | ↑↑ | ↓ | ↑↑↑ |
 Myopalladin | ↑↑∕↑↑↑ | ↑↑↑ | ↑∕↑↑ |
 Desmin | ↑↑↑ | (↑) | ↑↑↑ |
 Plectin | ↑ | ↓ | ↑↑↑ |
 Nestin | ↑∕↑↑ | - | ↑↑↑ |
 Syncoilin | ↑∕↑↑ | ↑↑↑ | ↑∕↑↑ |
Chaperone-assisted selective autophagy (CASA)/NBR1-mediated selective autophagy | |||
 BAG3 | ↑↑∕↑↑↑ | - | ↑↑↑ |
 HSPB8/Hsp22 | ↑↑ ∕ ↑↑↑ | ↑↑↑ | ↑↑↑ |
 HSPA8/Hsc70 | ↑↑ | ↑ | ↑↑↑ |
 p62 | ↑↑↑ | (↑)∕↑↑ | (↑) |
 NBR1 | ↑↑∕↑↑↑ | ↑ | ↑↑∕↑↑↑ |
Further chaperones | |||
 αB-crystallin | ↑∕↑↑ | ↑ | ↑↑↑ |
 HSPB1/Hsp27 | ↑∕↑↑ | ↑↑↑ | ↑↑↑ |
 Hsp70 | ↑↑ | ↑ | ↑↑↑ |
Unfolded protein response (UPR) / oxidative stress response/transcription regulation | |||
 BiP | ↑↑ | ↑↑ | (↑) |
 Thrombospondin 4 | ↑↑∕↑↑↑ | ↑↑↑ | ↑↑ |
 MGST3 | ↑↑↑ | - | ↑↑↑ |
 YBX3 | ↑ ∕ ↑↑ | ↑ | ↑ |
Actin dynamics | |||
 MURC | (↑) ∕ ↑↑ | (↑) | ↑↑↑ |
 MYBPH | (↑) ∕ ↑↑↑ | ↑↑↑ | (↑) |
 Tropomodulin 1 | ↑↑ ∕ ↑↑↑ | ↑↑↑ | (↑) |
 CSRP3 | ↑ | ↑↑ | ↑ |
Microtubule organization / vesicle transport | |||
 α-tubulin | ↑↑ | ↑ | ↑↑↑ |
 MAP4 | ↑↑ ∕ ↑↑↑ | (↑) | ↑↑↑ |
 PACSIN3 | (↑) ∕ ↑↑ | - | ↑↑↑ |
Sarcolemmal proteins | |||
 Dystrophin | ↑↑ | - | ↑↑ ∕ ↑↑↑ |
 Dysferlin | ↑↑ ∕ ↑↑↑ | ↑ | ↑↑ ∕ ↑↑↑ |
 Supervillin | ↑ ∕ ↑↑ | - | ↑↑↑ |
 δ-Sarcoglycan | (↑) | (↑) | (↑) |