Fig. 3
From: Diagnostically important muscle pathology in DNAJB6 mutated LGMD1D
a, c, d. Vastus lateralis muscle of a 72-year-old female (FF1, III-12): moderate or strong expression of proteins myotilin (a), desmin (c) and alphaB-crystallin (d) in the myofibrillar lesions with aggregates on immunohistochemistry. b. Congo red staining viewed through Texas-red filters shows numerous congophilic fluorescent deposits in muscle fibers. e. Dystrophin-2 showed ectopic expression of mild or moderate intensity in the same regions. f, g, h. The protein accumulations showing CASA complex proteins BAG3 (f), HSPB8 (g), and DNAJB6 (h)