Skip to main content

Table 1 Scoring of muscle damage based on pathology in muscle fibers

From: Lack of robust satellite cell activation and muscle regeneration during the progression of Pompe disease

Score Cross striation PAS-positive staining Vacuoles
 0 Normal None None
 1 >75 % normal Little in most and/or all Little in all and/or significant in some
 2 25–75 % normal Significant in all and strong in some; significant and/or strong in most Significant in all and/or many in some
 3 <25 % normal Very strong in all Many in all