Lack of robust satellite cell activation and muscle regeneration during the progression of Pompe disease

Table 1 Scoring of muscle damage based on pathology in muscle fibers

Score	Cross striation	PAS-positive staining	Vacuoles
0	Normal	None	None
1	>75 % normal	Little in most and/or all	Little in all and/or significant in some
2	25–75 % normal	Significant in all and strong in some; significant and/or strong in most	Significant in all and/or many in some
3	<25 % normal	Very strong in all	Many in all

ISSN: 2051-5960