Stage 2 | Stage 3 | Stage 4 | p-value | |
---|---|---|---|---|
Gender (M:F) | 5:3 | 10:6 | 6:3 | 0.628a |
Mean age at onset (SD) | 60 (9) | 58 (6) | 70 (8)* | 0.007b |
Mean age at death (SD) | 61 (9) | 61 (6) | 71 (8)* | 0.017b |
Mean duration since diagnosis (SD) | 1.5 (0.7) | 3.5 (1.7)* | 1.4 (0.6) | 0.002b |
Bulbar onset (N) | 3 | 4 | 2 | 0.904a |
Upper limb onset (N) | 2 | 6 | 3 | |
Lower limb onset (N) | 3 | 6 | 4 |