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Table 1 Clinical Data of cases studied

From: Dipeptide repeat protein inclusions are rare in the spinal cord and almost absent from motor neurons in C9ORF72 mutant amyotrophic lateral sclerosis and are unlikely to cause their degeneration

Case

Age

Sex

PMD

Diagnosis

1

73

M

42

ALS-TDP

2

70

F

27

ALS-TDP

3

60

M

70

ALS-TDP

4

44

F

24

ALS-TDP

5

68

M

5

ALS-TDP

mean ± SEM

63 ± 5

 

33 ± 11

ALS-TDP

6

59

F

35

ALS-C9 + ve

7

70

M

38

ALS-C9 + ve

8

59

M

46

ALS-C9 + ve

9

43

F

69

ALS-C9 + ve

10

53

M

82

ALS-C9 + ve

11

70

M

60

ALS-C9 + ve

12

55

M

76

ALS-C9 + ve

13

58

M

11

ALS-C9 + ve

14

64

M

68

ALS-C9 + ve

15

51

M

64

ALS-C9 + ve

mean ± SEM

58 ± 2

 

55 ± 5

 
  1. PMD post mortem delay (hours)