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Table 2 Summary of the five VPSPr cases used in this study

From: The prion protein protease sensitivity, stability and seeding activity in variably protease sensitive prionopathy brain tissue suggests molecular overlaps with sporadic Creutzfeldt-Jakob disease

VPSPr case number (in this study) PRNP-codon 129 genotype References Frozen tissues available (Abbreviations as in Figure5.) Semi-quantitative score for the presence of microplaques in the cerebellum 0 = absent 3+ = severe
1 VV This study FC, TC, PC, OC, Cb, Hip,Thal, Midbrain, Pons, Me 1+
2 VV [7] (Case 4) FC, Cb 3+
3 VV [7] (Case 3) FC, Cb, TC 1+
4 VV [5] FC, Cb 3+
5 MV [6] FC 0