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Table 2 Summated scores for DPR pathology ratings in Cortical, Medial Temporal, Motor, Subcortical and Cerebellar regions, as well as total score across all 5 regions, for patients with FTD (cases #1-8), FTD + MND (cases#9-14) and MND (cases#41-47) associated with expansion in C9ORF72

From: Brain distribution of dipeptide repeat proteins in frontotemporal lobar degeneration and motor neurone disease associated with expansions in C9ORF72

Case ID#   Summated DPR score
Pathology Cortex Medial temporal Motor Subcortical Cerebellar Total
1 FTLD-TDP A 16 12 3 3 5 39
2 FTLD-TDP A 12 14 3 1 5.5 35.5
3 FTLD-TDP A 15 18 3 5 7.5 48.5
4 FTLD-TDP A 13 12 2 2.5 3.5 33
5 FTLD-TDP A 12 11 1 3 3 30
6 FTLD-TDP A 11 9 1.5 3 2 26.5
7 FTLD-TDP A 12 9.5 1 5.5 3.5 31.5
8 FTLD-TDP A 22 23 2 4 5.5 55.5
9 FTLD-TDP B 20 15.5 2 1 4.5 43
10 FTLD-TDP B 12 11 2 2 4 31
11 FTLD-TDP B 11 10.5 2 1.5 4 29
12 FTLD-TDP B 18 16 3.5 4.5 5 47
13 FTLD-TDP B 11 11 2 3.5 2 29.5
14 FTLD-TDP B 16 15 3 4.5 6.5 45
41 MND 16 13 3 6 5.5 43.5
42 MND 15 13 3 3 1 35
43 MND 14 18 3 4 3 42
44 MND 12 18 2.5 5 3 40.5
45 MND 13 12 3 1.5 4.5 34
46 MND 11 19 2 4.5 3 39.5
47 MND 23 23 3 5 3.5 57.5