| Proposed nomenclature | |||||||||
---|---|---|---|---|---|---|---|---|---|---|
 | Current classificationb | PrPSctype | Transmission typec | Classification | Codon 129 genotype | PrPSctype | Histo-typed | Transmission type | Original PrPScstrain(s) | Existing PrPScstrain(s) |
Pure phenotypes | MM1 | 1 | M1CJD | MM1 | MM | 1 | S | M1 | M1 | M1 |
MM2C | 2 | M2CJD | MM2C | MM | 2 | C | ― | M2C | M2C | |
MV2C | 2 | N.D.e | MV2C | MV | 2 | C | N.D. f | M2C | M2C | |
MV2K | 2 | V2CJD | MVi + 2 | MV | i + 2 g | K | V2 | V2 | Mi + V2 | |
VV2 | 2 | V2CJD | VV2 | VV | 2 | P | V2 | V2 | V2 | |
Mixed phenotype | MV2K + C | 2 | N.D. | MVi + 2C | MV | i + 2 | K + C | V2 | M2C + V2 | M2C + Mi + V2 |