Table 2 Ratings for p62 and DPR antibody immunostaining of neuronal cytoplasmic inclusions for all 15 cases with expansions in C9ORF72
Case | CA4 | DG | GCC | |||||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Â | p62 | poly-GA | poly-GP | poly-GR | poly-PR | poly-AP | p62 | poly-GA | poly-GP | poly-GR | poly-PR | poly-AP | p62 | poly-GA | poly-GP | poly-GR | poly-PR | poly-AP |
1* | 2 | 2 | 3 | 3 | 0.5 | 0.5 | 1 | 2 | 0 | 0.5 | 0.5 | 0.5 | 4 | 4 | 3 | 0.5 | 0 | 0 |
2* | 3 | 3 | 2 | 3 | 0.5 | 1 | 2 | 2 | 0.5 | 2 | 0.5 | 1 | 2 | 3 | 3 | 0 | 0 | 0 |
3* | 3 | 3 | 3 | 2 | 0.5 | 0.5 | 4 | 3 | 3 | 0 | 0 | 0 | 1 | 4 | 2 | 2 | 0 | 0 |
4* | 2 | 2 | 3 | 3 | 0.5 | 0 | 3 | 2 | 3 | 0 | 0.5 | 0 | 3 | 3 | 3 | 0 | 0 | 0 |
5* | 2 | 1 | 3 | 3 | 0.5 | 0.5 | 3 | 3 | 2 | 0 | 0 | 0 | 2 | 3 | 3 | 1 | 0 | 0 |
6* | 1 | 2 | 2 | 1 | 0 | 0 | 1 | 2 | 2 | 0 | 0 | 0 | 1 | 1 | 1 | 0 | 0 | 0 |
7** | 3 | 3 | 3 | 3 | 0 | 0 | 3 | 3 | 2 | 0 | 0 | 0 | 4 | 4 | 4 | 0 | 0 | 0 |
8** | na | na | na | na | na | na | na | na | na | na | na | na | 1 | 1 | 1 | 0 | 0 | 0 |
9** | 3 | 2 | 3 | 3 | 0.5 | 0.5 | 1 | 2 | 1 | 0.5 | 0 | 0 | 0.5 | 3 | 1 | 0 | 0 | 0 |
10** | 3 | 2 | 2 | 2 | 0.5 | 0.5 | 4 | 3 | 3 | 1 | 0.5 | 0 | 3 | 3 | 2 | 0 | 0 | 0 |
11** | 3 | 3 | 3 | 3 | 0 | 0 | 4 | 3 | 2 | 2 | 0 | 1 | 0.5 | 3 | 2 | 1 | 0.5 | 0 |
12** | 3 | 3 | 2 | 3 | 0 | 0 | 4 | 3 | 1 | 1 | 0 | 0 | 1 | 3 | 3 | 1 | 1 | 0 |
13 | 0 | 2 | 2 | 2 | 0 | 0 | 0 | 2 | 2 | 0 | 0 | 0 | 1 | 1 | 1 | 0 | 0 | 0 |
14 | 3 | 2 | 3 | 3 | 0 | 1 | 1 | 2 | 2 | 0 | 0 | 0 | 3 | 4 | 2 | 0 | 0 | 0 |
15 | 1 | 1 | 1 | 1 | 0 | 0 | 2 | 2 | 2 | 2 | 0 | 0 | 1 | 1 | 1 | 0 | 0 | 0 |
16 | 2 | 2 | 2 | 0 | 0 | 0 | 2 | 2 | 2 | 2 | 0 | 0 | 3 | 3 | 3 | 0 | 0 | 0 |