Skip to main content

Table 2 Demographics, clinical syndrome and pathological subtypes assigned by 5 independent raters to FTLD-TDP cases in this study

From: Classification of FTLD-TDP cases into pathological subtypes using antibodies against phosphorylated and non-phosphorylated TDP43

Subtype

Case #

Age at death (y)/ Gender (M/F)

Disease duration (y)

Initial syndromes

pTDP43

iTDP43

     

Reviewer

Reviewer

     

1

2

3

4

5

1

2

3

4

5

A

1

76F

2

bvFTD

A

A

A

A

B

B

A

A

B

B

A

2

84F

8

Language FTD

C

A

A

C

C

A

A

A

C

A

A

3

54F

6

bvFTD

A

A

A

B

A

A

A

A

A

A

A

4

60M

3

Language FTD+bvFTD

A

A

A

A

A

A

A

A

A

A

A

5*

72M

9

bvFTD

A

A

A

A

A

A

A

A

C

A

A

6*

65M

2

bvFTD

A

C

A

C

A

A

C

C

B

A

A

7*

65F

3

bvFTD + MND

B

A

B

A

A

B

A

B

B

B

B

8*

55M

3

bvFTD

B

B

B

B

B

B

B

D

C

B

B

9

52F

1

bvFTD + MND

B

B

B

A

B

A

B

B

A

B

B

10

66M

2

bvFTD + MND

B

B

B

B

B

A

B

C

C

B

B

11

55F

2

bvFTD + MND

B

B

B

B

B

B

B

C

B

B

C

12

68F

1

Language FTD + MND

B

C

C

C

C

B

C

B

B

C

C

13

68M

12

bvFTD

C

C

C

C

C

C

C

C

C

C

C

14

83F

13

Language FTD

C

C

C

C

C

C

C

C

C

C

  1. * C9ORF72 gene mutation; bvFTD behavioral frontotemporal dementia; MND motor neuron disease.