Table 2 Study subject characteristics
Subject ID | Group | CK level (U/L) | Sex | Age at diagnosis | Rimmed vacuoles (%F) | LC3 (%FS) | p62 (%FS) | TDP-43 (%FS) |
|---|---|---|---|---|---|---|---|---|
1 | PM | 1,092 | M | 59 | 0.0 | 5.7 | 5.5 | 1.2 |
2 | PM | “1,000 s” | M | 85 | 0.0 | 6.0 | 10.0 | 0.5 |
3 | PM | 2,405 | F | 51 | 0.0 | 4.0 | 0.3 | 5.5 |
4 | PM | 1231 | M | 65 | 0.0 | 2.5 | 3.7 | 1.2 |
5 | PM | 1,497 | M | 47 | 0.0 | 1.7 | 11.0 | 0.2 |
6 | PM | 10,000 | M | 42 | 0.0 | 11.3 | 10.2 | 0.2 |
7 | PM | 477 | F | 66 | 0.0 | 3.8 | 4.0 | 0.5 |
8 | PM | 6,000 to 19,000 | M | 50 | 0.0 | 4.0 | 7.5 | 1.2 |
9 | PM | 3,000 | M | 59 | 0.0 | 6.7 | 8.3 | 0.8 |
10 | PM | 834 | M | 53 | 0.0 | 2.7 | 19.2 | 0.3 |
11 | PM | 2,300 | M | 43 | 0.0 | 2.7 | 4.0 | 0.2 |
12 | PM | 1,000 to 4,000 | M | 50 | 0.0 | 2.0 | 2.8 | 0.2 |
13 | IBM | 515 ( 1 y before biopsy) | F | 64 | 2.7 | 31.0 | 18.5 | 8.5 |
14 | IBM | 5,201 | F | 75 | 1.2 | 19.5 | 18.0 | 1.0 |
15a | IBM | 700 | F | 57 | 1.0 | 24.0 | 20.0 | 12.5 |
16a | IBM | 444 | M | 62 | 4.3 | 29.5 | 59.5 | 40.5 |
17 | IBM | 547 | M | 77 | 2.5 | 15.5 | 16.5 | 9.0 |
18 | IBM | NA | F | 74 | 1.5 | 16.0 | 9.2 | 2.8 |
19 | IBM | 235 (5 y before biopsy) | F | 73 | 3.0 | 34.0 | 32.5 | 16.0 |
20a | IBM | 576 to 732 | F | 69 | 4.5 | 48.5 | 43.5 | 27.5 |
21 | IBM | NA | M | 75 | 3.0 | 11.0 | 22.5 | 18.5 |
22 | IBM | 900 | M | 59 | 2.2 | 33.5 | 36.0 | 16.0 |
23a | IBM | 700 | M | 66 | 0.7 | 9.0 | 15.0 | 1.8 |
24 | IBM | NA | M | 76 | 0.5 | 32.5 | 12.0 | 0.2 |
25 | PM-COX | NA | M | 54 | 0.0 | 2.7 | 4.8 | 1.3 |
26 | PM-COX | 121 | F | 71 | 0.0 | 3.7 | 7.7 | 4.7 |
27 | PM-COX | 802 | F | 55 | 0.0 | 6.0 | 6.3 | 0.2 |
28 | PM-COX | 1,254 to 2,093 | F | 85 | 0.0 | 10.0 | 4.7 | 0.5 |
29a | PM-COX | 395 | M | 75 | 0.0 | 13.7 | 13.8 | 1.0 |
30 | PM-COX | 174 to 229 | M | 54 | 0.0 | 3.8 | 8.0 | 1.0 |
31 | PM-COX | NA | F | 76 | 0.0 | 4.3 | 8.8 | 4.2 |
32 | PM-COX | 2,000 to 3,000 | F | 58 | 0.0 | 3.3 | 1.5 | 0.7 |
33a | PM-COX | NA | M | 59 | 0.0 | 15.5 | 22.5 | 16.0 |
34 | PM-COX | NA | F | 63 | 0.0 | 16.5 | 28.5 | 4.5 |
35a | PM-COX | 871 | M | 64 | 0.0 | 47.5 | 30.5 | 0.5 |
36 | PM-COX | 74,600 | F | 58 | 0.0 | 2.3 | 2.3 | 0.2 |
37 | PM-COX | 339 to 789 | F | 65 | 0.0 | 4.7 | 3.0 | 2.5 |
38 | pIBM | 6,500 | F | 42 | 0.0 | 3.8 | 12.8 | 1.2 |
39 | pIBM | 6,000 to 12,000 | F | 58 | 0.0 | 33.0 | 32.0 | 0.5 |
40 | pIBM | 802 | F | 71 | 0.0 | 5.3 | 2.5 | 0.3 |
41 | pIBM | 7,090 | F | 55 | 0.0 | 16.5 | 34.5 | 0.7 |
42 | pIBM | 74,000 | F | 61 | 0.0 | 18.5 | 10.5 | 4.2 |
43a | pIBM | 871 | M | 62 | 0.0 | 25.5 | 10.5 | 6.5 |
44 | pIBM | 4,580 | F | 30 | 0.0 | 74.0 | 58.5 | 1.3 |
45 | pIBM | NA | F | 75 | 0.0 | 15.5 | 5.5 | 0.5 |
46a | pIBM | 840 | M | 64 | 0.0 | 17.0 | 21.0 | 12.0 |
47 | pIBM | 10,000 | M | 53 | 0.0 | 16.0 | 15.3 | 1.2 |
48 | pIBM | 864 | F | 44 | 0.0 | 6.7 | 4.5 | 0.0 |
49 | pIBM | 600 | F | 83 | 0.0 | 24.7 | 2.5 | 0.3 |
50 | pIBM | 293 | M | 68 | 0.0 | 7.3 | 4.8 | 1.3 |
51 | pIBM | 6,000 | F | 50 | 0.0 | 21.5 | 17.0 | 0.8 |
52a | pIBM | 222 (4 y after biopsy) | M | 79 | 0.0 | 17.5 | 22.5 | 3.3 |
53 | pIBM | NA | M | 58 | 0.0 | 7.2 | 2.5 | 2.5 |