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Table 1 Case characteristics

From: Phenotypically concordant distribution of pick bodies in aphasic versus behavioral dementias

Case

Sex

PMI (h)

Age at Death (Years)

Disease Duration (Years)

Brain weight (g)

Education (years)

Clinical Dx

PPA Subtype

ApoE

Comorbid pathologic diagnoses

1

F

25

78

12

1010

20

bvFTD

–

3,4

Moderate vascular disease, Low ADNC (A0,B1,C1)

2

M

21

67

8

990

20

bvFTD

–

2,3

Vascular disease

3

F

2

71

14

661

18

bvFTD

–

3,3

Mild vascular disease

4

F

13

58

12

866

12

bvFTD

–

2,3

Low ADNC (A0,B1,C0), Fahr’s

5

F

9

82

12

890

18

bvFTD

–

3,3

Low ADNC (A2,B1,C2), moderate vascular disease

6

M

24

70

11

1105

12

bvFTD

–

3,3

Low ADNC (A1,B1,C2), moderate vascular disease

7

M

7

66

6

988

14

bvFTD

–

UNK

Low ADNC (A1,B0,C2), mild vascular disease

8

M

24

61

14

880*

18

bvFTD

–

UNK

Unilateral hippocampal sclerosis, moderate vascular disease

9

M

49

69

7

1133

16

bvFTD

–

3,3

Low ADNC (A2,B0,C1), mild to moderate vascular disease

10

M

5

70

14

1018

20

PPA

G

3,3

Mild vascular disease, Low ADNC (A0,B1,C0)

11

F

28

64

11

990

16

PPA

S

3,4

Hippocampal sclerosis, moderate vascular disease

12

M

UNK

65

12

1055

14

PPA

G

3,3

Moderate vascular disease

13

M

27

75

9

1125

14

PPA

Other – Mixed

UNK

Low ADNC (A3,B1,C3), mild atherosclerosis

14

F

UNK

67

4

1140*

12

PPA

G

3,4

Low ADNC (A2,B1,C3), 2 acute parenchymal hematomas, moderate vascular disease

15

M

5

69

7

1100

12

PPA

Other – Severe

3,3

Moderate vascular disease, left temporal pole subacute infarct, low ADNC (A1,B0,C1)

16

F

3.5

76

12

965

16

PPA

G

3,4

Moderate vascular disease

17

F

14

68

8

1010

16

PPA

G

3,3

Mild vascular disease, low ADNC (A3,B0,C2)

18

F

24

71

14

1226

17

PPA

G

3,3

Moderate vascular disease

  1. bvFTD Behavioral variant frontotemporal dementia, PPA Primary progressive aphasia, M Male, F Female, PMI Postmortem interval, UNK Unknown, *Fixed, ApoE Apolipoprotein E, G Agrammatic, S Semantic, ADNC Alzheimer’s disease neuropathologic change