Skip to main content

Table 2 Clinical information relating to lymphoblastoid cell lines derived from ALS patients

From: A data-driven approach links microglia to pathology and prognosis in amyotrophic lateral sclerosis

ID

Gender

Age at onset (years)

Disease duration (years)

Site of onset

C9ORF72 status

Familial/Sporadic

1

F

28

1.10

Bulbar

+

Familial

2

F

57

1.21

Mixed

+

Familial

3

F

62

0.17

Bulbar

+

Familial

4

M

59

<1 year

N/A

+

Familial

5

M

63

1.71

Mixed

+

Familial

6

M

47

1.63

Limb

+

Familial

7

F

51

0.97

Bulbar

+

Familial

8

M

60

1.15

Bulbar

+

Sporadic

9

M

68

1.56

Limb

+

Sporadic

10

F

37

1.74

Limb

+

Sporadic

11

M

56

2.20

Limb

+

Sporadic

12

M

45

1.47

Limb

+

Sporadic

13

M

72

0.52

Limb

+

Sporadic

14

F

58

1.33

Mixed

+

Sporadic

15

M

47

1.57

Limb

+

Sporadic

16

M

64

0.66

Limb

+

Sporadic

17

M

62

1.96

Limb

+

Sporadic

18

M

65

1.40

Limb

+

Sporadic

19

F

69

>4 years

Limb

+

Familial

20

M

63

>5 years

Limb

+

Familial

21

F

64

6.92

Limb

+

Familial

22

F

56

4.14

Limb

+

Familial

23

F

72

4.66

Limb

+

Sporadic

24

F

48

5.95

Limb

+

Sporadic

25

F

37

4.50

Bulbar

+

Sporadic

26

M

61

~4 years

Mixed

+

Sporadic

27

M

44

0.94

Mixed

-

Sporadic

28

M

54

5.90

Limb

-

Sporadic

29

M

72

5.99

Limb

-

Sporadic

30

M

76

0.85

Limb

-

Sporadic

31

F

76

1.08

Bulbar

-

Sporadic

32

F

65

1.10

Limb

-

Sporadic

33

M

65

7.70

Limb

-

Sporadic

34

M

49

0.39

Limb

-

Sporadic

35

M

32

6.05

Limb

-

Sporadic

36

M

35

6.85

Limb

-

Sporadic

37

F

62

0.73

Bulbar

-

Sporadic

38

F

58

6.02

Limb

-

Sporadic

39

M

66

0.85

Limb

-

Sporadic

40

M

82

6.67

Limb

-

Sporadic

41

F

75

0.89

Limb

-

Sporadic

42

M

49

0.70

Limb

-

Sporadic

43

F

68

6.17

Limb

-

Sporadic

44

F

62

6.69

Limb

-

Sporadic

45

M

71

7.12

Limb

-

Sporadic

46

M

86

1.04

Limb

-

Sporadic

  1. C9ORF72 status indicates the presence (+) or absence (-) of a GGGGCC-repeat expansion in the C9ORF72 gene
  2. M Male, F Female